Cystadane (Betaine Anhydrous) is used in children and adults for the treatment of homocystinuria. This is used to decrease high homocysteine blood levels. Homocystinuria is a rare genetic disorder in which there is an abnormal accumulation of the amino acid homocysteine in the urine and blood. Included within the category of homocystinuria are:
- Cobalamin cofactor metabolism (cbl) defect
- Cystathionine beta-synthase (CBS) deficiency
- 5,10-methylenetetrahydrofolate reductase (MTHFR) deficiency
How does Cystadane (Betaine Anhydrous) work?
Cystadane (Betaine Anhydrous) helps in the metabolism of a chemical called homocysteine. Homocysteine is involved in the usual task of many different parts of the body, including muscles, bones, blood, eyes, nerves, heart, and the brain. This medication prevents the build-up of homocysteine in the blood. Levels of homocysteine are very high in some people who have problems with their metabolism.
Why use Cystadane (Betaine Anhydrous)?
Cystadane (Betaine Anhydrous) is an agent for the treatment of homocystinuria. It contains no ingredients other than Betaine Anhydrous. Cystadane is hygroscopic powder, white, and granular. In which it is diluted in water and administered orally. This treatment has been approved by the U.S. Food and Drug Administration (FDA).
How to use Cystadane (Betaine Anhydrous)?
The usual dosage in pediatric and adult patients is 6 grams per day. It should be administered orally in divided doses of 3 grams twice daily. In pediatric patients 3 years of age below, dosage may be started at 100 mg/kg/day. It is divided into twice daily doses and then increased weekly by 50 mg/kg.
The recommended amount of Cystadane (Betaine anhydrous) should be measured with the measuring scoop provided. It is one level 1.7 mL scoop is equal to 1 gram of Betaine anhydrous powder. Then dissolved in 4 to 6 ounces (120 to 180 mL) of water, milk, and juice or mixed with food for instant ingestion.
What are the side-effects of Cystadane (Betaine Anhydrous)?
- Stomach upset
- Unusual body odor
- Unpleasant taste in your mouth
Call your doctor if you have:
- Memory problems
- Muscle weakness
- Vision changes
- Changes in your mental taste
- Decreased consciousness
- Problems with speech, balance, or walking
Warnings and Precautions
- Let your doctor know if you have any allergies, medical history, or current treatments.
- If you are pregnant or breastfeeding women, consult your doctor first.
- Call for medical help if there is a symptom of allergic reaction (difficulty breathing, hives, and swelling of your lips, tongue, face, or throat).